porphobilinogen synthase

Type:Term

Definitions
1. a liver enzyme catalyzing the formation of porphobilinogen and water from two molecules of ΄-aminolevulinate, an important reaction in porphyrin biosynthesis; inhibited by lead in cases of lead poisoning; a deficiency of this enzyme results in elevated levels of ΄-aminolevulinate and results in neurologic disturbances.

Synonyms
΄-aminolevulinate dehydratase

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