Definition: 'Usher Syndrome'
Usher syndromeType: Term
1. autosomal recessive inheritance with genetic heterogeneity; based on gene cloning and location, six forms of type I cause sensorineural hearing loss, loss of vestibular function, and retinitis pigmentosa; three forms of type II and one form of type III are characterized by hearing loss and retinitis pigmentosa.
The information shown above for Usher syndrome is provided by Stedman's.
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